Miscellaneous
Arrhythmogenic right ventricular dysplasia: from genetics to treatment
1Division of Cardiology St. Luke’s - Roosevelt Hospital Center Columbia University, College of Physicians & Surgeons New York City, NY, USA
2Division of Pre-Exercise Heart Screening Program St. Luke’s - Roosevelt Hospital Center Columbia University, College of Physicians & Surgeons New York City, NY, USA
3Division of Cardiology, Department of Medicine, St. Luke’s-Roosevelt Hospital Center, Columbia University, College of Physicians and Surgeons, New York, NY, USA
2Division of Pre-Exercise Heart Screening Program St. Luke’s - Roosevelt Hospital Center Columbia University, College of Physicians & Surgeons New York City, NY, USA
3Division of Cardiology, Department of Medicine, St. Luke’s-Roosevelt Hospital Center, Columbia University, College of Physicians and Surgeons, New York, NY, USA
Anatol J Cardiol 2009; (9): 24-31 PubMed ID: 20089484
Abstract
Arrhythmogenic right ventricular dysplasia (ARVD), also known as arrhythmogenic right ventricular cardiomyopathy, is a genetic cause for sudden cardiac arrest. In ARVD, there is progressive replacement of normal myocytes, with fat and fibrous tissue, predominantly in the right ventricle that predisposes the individual to arrhythmias. Patients who are identified with this condition are risk stratified; those at high risk are recommended to have implanted cardioverter defibrillators
Keywords: Arrhythmogenic right ventricular dysplasia, implantable cardioverter defibrillator, sudden cardiac death